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Argininosuccinase (medicine)


argininosuccinase -->
argininosuccinate lyase
<enzyme> An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease argininosuccinic acidemia in man.

Chemical name: N-(L-Argininosuccinate) arginine-lyase

Registry number: EC 4.3.2.1