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See Also: branched chain ketonuria(medicine)
branched chain ketoaciduria(medicine)
amino acids, branched-chain(medicine)
branched chain acyl-CoA oxidase(medicine)
Amino acid, branched-chain(health)
branched-chain fatty acid synthetase(medicine)
branched-chain fatty-acid-kinase(medicine)
2-methyl branched-chain enoyl-CoA reductase(medicine)
Ketonuria(health)
ketonuria(medicine)

branched chain ketonuria (medicine)


branched chain ketonuria -->
maple syrup urine disease
Hereditary disease due to deficiency of an enzyme involved in amino acid metabolism, characterised by urine that smells like maple syrup.


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